Intraoperative cytodiagnosis of ciliary body medulloepithelioma masquerading as anterior ciliary staphyloma.

摘要

Intraocular medulloepithelioma (previously known as diktyoma or teratoneuroma) is an embryonic neoplasm that most often occurs in the ciliary body and rarely in the iris, retina or optic nerve.This neoplasm is characteristically a disease of childhood and usually becomes apparent clinically during the first decade of life. A small medulloepithelioma in the ciliary body region of the eye may occasionally be asymptomatic and extremely difficult to detect on clinical examination. Familiarity with the clinical appearance of intraocular medulloepithelioma is the most reliable feature in the diagnosis. In case of an unusual presentation and in the absence of sophisticated ancillary studies, a transocular fine needle aspiration cytology (FNAC) or squash smears are recommended and are helpful in the diagnosis of difficult cases.Cytologic specimens from the eye' in the form of fine needle aspirates, intraocular (vitrectomy) washings and intraoperative squash specimens are utilized for the diagnosis of neoplastic and nonneoplastic conditions.We present one such case where intraoperative cytology helped in reaching the final diagnosis of medulloepithelioma.