Mitral repair in children with connective tissue disorders:On the edge, over the edge, or edge-to-edge?

摘要

Mitral valve repair in patients with connective tissue disorders (CTDs) is challenging. The earlier in life that a repair has to be performed, the more difficult it is, because CTD that manifests in childhood represents the most severe end of the disease spectrum.1 Whereas in adults with CTD mitral valve repair can be achieved with similar outcomes to those with myxomatous mitral valve disease,2 the outcomes of mitral valve repair in children with CTD remain uncertain.1 The literature on the topic is sparse, with only a few small series, which report high rates of valve replacement.