Os Odontoideum

摘要

Introduction: "Os odontoideum" is a rare craniovertebral junction disease that presents itself as a dystopic ossicle from a hy-poplastic C2 dens, contributing to a craniocervical instability.Objectives and Methods: We report a 45-year-old woman harboring a dystopic os odontoideum, who sustained a progressive neurological deterioration with marked circumferential spinal cord compression. She was subjected to a prior posterior sub-occipital craniectomy with occipitocervical fixation, followed by an anterior transoral-transpharyngeal odontoidectomy.Results and Discussion: Both procedures were performed uneventfully, and the patient had a remarkable improvement afterward. We believe that our step-wise surgical management to os odontoideum is feasible and accomplishes excellent outcomes.