Congenital Ventral Hernia in Association with Focal Dermal Hypoplasia

摘要

Abstract:Focal dermal hypoplasia is a rare, X‐linked dominant syndrome characterized by dysplasla of the skin, skeleton, and central nervous system. We report an intant who was born with severe focal dermal hypoplasla and an epigastric hernia. Operative timing and approach to abdominal wall defects in the presence of severe cutaneous dysplasia are discusse