Surgical Decision-Making in Spinal Instability in Facioscapulohumeral Muscular Dystrophy Related with a Spinal Muscle Atrophy

摘要

Theindication and treatment of degenerativespinal pathology arespecificto the preparation ofthe neurosurgeon specialist. However, thereisagenerallack ofinformation on the possiblesurgicalindication in patients suffering fromrare genetic pathologies, such as myopathies, which candeterminespinal deformities in adulthood. Facioscapulohumeralmuscular dystrophy (FSHD) represents one ofthe mostcommon geneticmyopathiescharacterized byweakness ofthefacialand periscapular musculature.