Transcatheter Decompression of the Left Atrium in an Adolescent with a Double Inlet Left Ventricle, Severe Parachute Mitral Valve Stenosis and Pulmonary Hypertension

摘要

A 17-year style="font-family:Verdana;">-old style="font-family:Verdana;"> adolescent with non-operated double inlet left-ventricle and severe stenosed parachute mitral valve is reported. He style="font-family:Verdana;">was style="font-family:Verdana;">admitted with repetitive syncope related to intermittent atrial fibrillation. Life-threatening syncope combined with pre- style="font-family:Verdana;"> style="font-family:Verdana;">and post style="font-family:Verdana;">- style="font-family:Verdana;">capillary pulmonary hypertension together with his single ventricle pathophysiology led to the decision for left atrial decompression by percutaneous static atrial septum ballooning after transseptal needle perforation. Aiming to create a restrictive atrial septum defect, unloading of the left atrium without disturbing the balanced hemodynamics was directed for a long-term palliation or as a basis for a further surgical follow-up approach.