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Development and Treatment of Tertiary Hyperparathyroidism in Patients with Pseudohypoparathyroidism Type 1B

机译:1B型假性甲状旁腺功能减退症的发展和治疗

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Context:Pseudohypoparathyroidism type 1B (PHP1B) patients have PTH resistance at the renal proximal tubule and develop hypocalcemia and secondary hyperparathyroidism. Hyperparathyroid bone disease also develops in some patients. PHP1B patients are at theoretical risk of developing tertiary hyperparathyroidism.
机译:背景:假性甲状旁腺功能低下的1B型(PHP1B)患者在肾近端小管具有PTH抵抗力,并发生低血钙和继发性甲状旁腺功能亢进。甲状旁腺功能亢进症也发生在某些患者中。理论上,PHP1B患者有发展为第三甲状旁腺功能亢进症的风险。

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