Purpose:The aim of this study was to assess treatment and outcome with respect to clinical and pathological features.Patients and methods:Thirty-nine patients were identified (range 7–66 years, mean 23). Initial treatment comprised localexcision in 11 patients and wide excision in 14. Post-operative external beam radiotherapy was prescribed in 22 patientswith a total dose of 60 Gy, delivered in two phases.Results:The cause-specific survival for the entire group was 79, 63, 56 and 45% at 1, 3, 5 and 10 years, respectively. A distallimb location was associated with a better prognosis than proximal limb location (P= 0.04).Conclusions:Our data favour treatment with wide functional excision followed by radical dose radiotherapy in attempt tominimize risk of local recurrence, especially when primary tumours are bigger than 3 cm. Our data also suggest the sametreatment for local recurrence, when technically possible, to avoid amputation.
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