Ameloblastic Fibrosarcoma of Mandible in a Paediatric Patient- A Rare Case Report

摘要

Background: Ameloblastic fibro sarcoma is a tumour of odontogenic origin. It is frequently seen in the 3~(rd) and 4~(th) decade of life. Case report: We report a case of 17 years old female who presented with left lower jaw swelling. CT scan revealed a large expansile osteolytic soft tissue mass in mandible. The patient underwent left extended hemimandibulectomy. Grossly the large mass measured 16x9x6.5cm, destructing the underlying mandible. Microscopic examination revealed a biphasic tumor composed of islands of benign odontogenic epithelium in abundant mesenchymal component, mild nuclear pleomorphism, and occasional mitosis. Hence the diagnosis of Ameloblastic Fibrosarcoma- Low grade was made. On radiological and clinical follow up patient is free of tumor till date. Conclusions: Ameloblastic fibrosarcoma is rare tumor of paediatric age. Surgical excision is a treatment of choice.