Prader-Willi ??? ???? sugammadex? ??? ????? ?? - ?? ?? -

摘要

We treated a 4-year-old patient with a genetic disorder, Prader–Willi syndrome, that was accompanied by pulmonary hypertension due to upper airway obstruction. Prader–Willi syndrome is a complex genetic condition characterized by hypotonia, feeding difficulties, poor growth, and delayed development. Hypotonia was the main concern in the anesthetic management of this patient, including the choice of a neuromuscular blocking agent. We report successful induction of anesthesia in this patient with sevoflurane inhalation, remifentanil infusion, and a non-depolarizing muscle relaxant, rocuronium, while following up the status of the neuromuscular block by train-of-four monitoring and reversing the neuromuscular block with sugammadex.