Pancreatic Ewings Sarcoma- A Dreadful Tumor

摘要

Extraosseous Ewing’s sarcoma/primitive neuroectodermal tumor (ES/PNET) is an uncommon, aggressive, and malignant tumor with poor outcome. Pancreas in one of the very rare extraosseous location for this tumor thus minimal information regarding this disorder is present in literature. The present case was clinically and radiologically misdiagnosed as a pancreatic tumor. Histopathology of the tumor tissue revealed “small round cells” that were positive for CD99 (MIC-2), confirming the diagnosis of ES/PNET. This case report emphasis on the importance of considering Ewing’s sarcoma in the differential diagnosis of intraabdominal, extraintestinal masses particularly in young patients presenting with pancreatic mass.