首页> 美国卫生研究院文献>Pathology Research International >Left-Sided Congenital Diaphragmatic Hernia with Multiple Congenital Cardiac Anomalies Hernia Sac and Microscopic Hepatic Heterotopia: A Case Report
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Left-Sided Congenital Diaphragmatic Hernia with Multiple Congenital Cardiac Anomalies Hernia Sac and Microscopic Hepatic Heterotopia: A Case Report

机译:左侧先天性ph肌疝伴多发性先天性心脏异常疝囊和镜下肝异位症:一例报告

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摘要

Congenital diaphragmatic hernia is a common congenital anomaly of uncertain etiology. Its association with multiple congenital anomalies in various organs is well recognized and antenatal radiological evidence of congenital diaphragmatic hernia warrants thorough evaluation to detect other anomalies, some of which can be life threatening. Rarely, heterotopic hepatic tissue is identified in the hernia, a rare pathological finding, exhibiting more than one macroscopic and microscopic characteristics, and always associated with cardiac congenital anomalies. Herein, we report a case of left-sided microscopic heterotopic hepatic tissue in a congenital diaphragmatic hernia in an infant with multiple cardiac congenital anomalies, but with preserved pericardium.
机译:先天性diaphragm肌疝是病因不明的常见先天性异常。它与各个器官的多个先天性异常的关联得到了公认,并且先天性diaphragm肌疝的产前放射学证据值得进行彻底评估以检测其他异常,其中一些异常可能危及生命。很少在疝气中发现异位肝组织,这是一种罕见的病理学发现,表现出一种以上的宏观和微观特征,并且总是与心脏先天性异常有关。本文中,我们报告了多发性先天性异常但心包保留的婴儿先天性diaphragm疝的左侧微观异位肝组织。

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