Fatty Liver and Autoimmune Hepatitis: Two Forms of Liver Involvement in Lipodystrophies

摘要

IntroductionLipodystrophies are a heterogeneous group of rare diseases (genetic or acquired) characterized by a partial or generalized deficit of adipose tissue, resulting in less energy storage capacity. They are associated with severe endocrine-metabolic complications with significant morbidity and mortality. In the pathogenesis of the acquired forms, immunological disorders may be involved.